Circular Shunt after Cardiac Surgery in Pulmonary Atresia with Intact Ventricular Septum

Authors

Keywords:

pulmonary atresia; cyanosis; interventricular septum.

Abstract

Circular shunt is a rare situation where there is a short circuit, in which blood reaches the cardiac chamber itself without passing through the pulmonary or systemic capillary bed. Different variables, mainly anatomical, are involved in its development, which allow the existence of this intracardiac circulation. However, it seems that right ventricular dysfunction may be one of the most decisive variables. In order to recognize the deleterious impact of circular shunt physiology and the importance of echocardiography for its diagnosis, we describe the case of a newborn infant diagnosed with pulmonary atresia with an intact interventricular septum, a right ventricle with dysplastic inflow and a severely hypertrophic right ventricle. Atrioseptectomy, modified Blalock-Taussig fistula and pulmonary commissurotomy were performed. Postoperative evolution was torpid with manifestations of systemic hypoperfusion, generalized o edema, oligoanuria, metabolic acidosis, hyperlactatemia and progressive hypoxemia. Echocardiographic evaluation demonstrated circular shunt physiology. The resulting multi-organ failure ended the patient's life.

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References

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Published

2024-12-08

How to Cite

1.
Bravo Pérez de Ordaz L, Ceruto-Ortiz LA. Circular Shunt after Cardiac Surgery in Pulmonary Atresia with Intact Ventricular Septum. Rev. cuba. cardiol. cir. cardiovasc. [Internet]. 2024 Dec. 8 [cited 2026 Mar. 7];30:e2306. Available from: https://revcardiologia.sld.cu/index.php/revcardiologia/article/view/2306

Issue

Vol. 30 (2024): Publicación continua

Section

Case Presentation

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